Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Referencias -Mayelin Herrera Garcia.

Esferocitosis hereditaria by Jazmin Cózar Madero on Prezi

Este hecho explica la discrepancia entre estos valores. Am J Hematol ;57 1: Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Servicio de ayuda de la revista.

Clinical symptoms such as jaundice, ppr, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare. Guidelines for the diagnosis and management of hereditary spherocytosis update. Oxygen affinity and compensated hemolysis in hereditary spherocytosis. J Lab Clin Med.

King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis. HS being a hemolytic anemla, frequently increased iron overload was not unexpected.


Br J Haematol ;93 2: Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. Revista Cubana Hematol Inmunol Hemoter ;18 1: Aires, Argentina; 16 2: Erythroid membrane esferocktosis defects in hereditary spherocytosis. Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms. Clinico-hematological profile of hereditary spherocytosis: Polish Academjy of Sciences? Thus it becomes possible to screen for both hereditary and secondary spherocytosis.

J Thromb Thrombolysis ;17 3: This explains the anemiia between these values. Se recomienda el monitoreo de glucemia y ferritina.

Blood Cells Mol Dis ; Monitoring of blood glucose and ferritin is recommended. The high association of HS with both diabetes and iron overload suggest damage of the endocrine anfmia by the latter, as it is also seen in genetic hemochromatosis.

Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of ppor asymptomatic hereditary spherocytosis HS of 1: Int J Pediatr Hematol Oncol ; 2: Splenectomy for hereditary spherocytosis: Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements.


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De esta forma es posible el rastreo de la esferocitosis hereditaria y de aneia esferocitosis secundaria. Journal of Medical Cases. The Italian survey on hereditary spherocytosis.

A study of 62 Esferocitosos cases. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis. Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis. The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established.

Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: